Littoral cell angioma of the spleen accompanied by haemophagocytic syndrome in a dialysis patient suffering from aa amyloidosis

Authors

  • Theofanis Apostolou
  • George Tsagalis
  • Dimitra Rontogianni
  • Georgia Kourti
  • George Metaxatos
  • Christalleni Christodoulidou
  • Valsamakis Hadjiconstantinou

DOI:

https://doi.org/10.2015/hc.v2i3.38

Keywords:

AA amyloidosis Littoral cell angioma, Spleen, Haemophagocytic syndrome, Haemodialysis.

Abstract

Littoral cell angioma (LCA) is a rare form of vascular tumor unique to the spleen that arises from the specialized endothelial cells that line the splenic sinuses (littoral cells). Haemophagocytic syndrome (HS) is also a rare hematologic disorder that some times accompanies LCA. The authors describe a young dialysis patient with a history of familiar mediteranean fever and secondary amyloidosis who was found to have this rare association of AA amyloidosis with LCA and haemophagocytic syndrome.

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Issue

Vol. 2 No. 3 (2007)

Section

CASE REPORTS

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